Oral management of Marfan syndrome: an overview and case report.

نویسندگان

  • Esdras Campos França
  • Lucas Guimarães Abreu
  • Saul Martins Paiva
  • Alexandre Fortes Drummond
  • Maria Esperanza Cortes
چکیده

Marfan syndrome is an autosomal-dominant genetic disorder that affects connective tissues. Diagnosis is based on genetic history as well as major and minor clinical criteria. This article presents a case of Marfan syndrome, emphasizing the clinical manifestations of the disease, and provides an overview of oral management. Knowledge of the etiopathologic and clinical aspects of this condition is essential to providing dental treatment aimed at improving the quality of life of affected individuals.

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عنوان ژورنال:
  • General dentistry

دوره 64 6  شماره 

صفحات  -

تاریخ انتشار 2016